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An Unusual Presentation of Mastocytosis: Unilateral Swelling of the Vulva
Author(s) -
Roy Joydip,
Metry Denise W.,
Hicks John,
Morgan Alice J.,
Heptulla Rubina A.
Publication year - 2005
Publication title -
pediatric dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 73
eISSN - 1525-1470
pISSN - 0736-8046
DOI - 10.1111/j.1525-1470.2005.00139.x
Subject(s) - medicine , vulva , presentation (obstetrics) , dermatology , anatomy , surgery
Mastocytosis is a primary, abnormal accumulation of mast cells associated with a broad range of local and systemic symptoms. We report two female adolescents with episodic, unilateral, swelling of the labia majora that was discovered to be an unusual presentation of mastocytosis. Mastocytosis is frequently misdiagnosed because of its rarity and variable clinical presentation, which often mimics other conditions. In the appropriate setting, mastocytosis should be included in the differential diagnosis of labium majus swelling.