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Childhood Vulval Lichen Sclerosus in a Patient with Ectodermal Dysplasia and Uncombable Hair
Author(s) -
Powell Jenny,
Wojnarowska Fenella,
Dawber Rodney,
Slavotinek Anne,
Huson Susan
Publication year - 1998
Publication title -
pediatric dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 73
eISSN - 1525-1470
pISSN - 0736-8046
DOI - 10.1111/j.1525-1470.1998.tb01392.x
Subject(s) - ectodermal dysplasia , lichen sclerosus , medicine , dermatology , atopy , girl , cabello , pathology , biology , scalp , immunopathology , genetics
An 11‐year‐old girl was diagnosed as having ectodermal dysplasia, with abnormalities of her nails, teeth, and hair noted from infancy. Her hair was unruly and investigations confirmed the changes seen in “cheveux incoiffables”—the uncombable hair syndrome. She also had atopy requiring treatment to control asthma and eczema. When she was 8 years old she developed vulval lichen sclerosus, which was controlled easily with early treatment. The coexistence of these conditions is discussed.