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Dermatofibrosarcoma Protuberans in Childhood
Author(s) -
BouyssouGauthier MarieLaure,
Labrousse François,
Longis Bernard,
Bedane Christophe,
Bernard Philippe,
Bonnetblanc JeanMarie
Publication year - 1997
Publication title -
pediatric dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 73
eISSN - 1525-1470
pISSN - 0736-8046
DOI - 10.1111/j.1525-1470.1997.tb00691.x
Subject(s) - dermatofibrosarcoma protuberans , medicine , dermatology , presentation (obstetrics) , localized scleroderma , radiology , lichen sclerosus
Dermatofibrosarcoma protuberans (DFSP) is a rare cutaneous tumor with a possibly misleading presentation. It is rare in childhood. We report an 18‐month‐old child with an acquired atrophic plaque of the left ankle. Based on clinical findings, initial proposed diagnoses included localized scleroderma and localized lipoatrophy. At the age of 5 years the plaque had increased in size and become a purplish color. Several firm nodules were seen at its periphery. A diagnosis of DFSP was proposed and confirmed histologically. A large surgical resection was performed. This case illustrates that DFSP may occur In childhood, during which initial diagnosis is generally more difficult than in adulthood.