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Pachydermodactyly in Two Young Girls
Author(s) -
Bardazzi Federico,
Neri Iria,
Fanti Pier Alessandro,
Patrizi Annalisa
Publication year - 1996
Publication title -
pediatric dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 73
eISSN - 1525-1470
pISSN - 0736-8046
DOI - 10.1111/j.1525-1470.1996.tb01241.x
Subject(s) - tuberous sclerosis , medicine , girl , ehlers–danlos syndrome , young adult , dermatology , disease , pediatrics , pathology , developmental psychology , psychology
Pachydermodactyly is a benign, superficial fibromatosis frequently observed in young males. We describe the condition in two young girls affected by Ehlers‐Danlos syndrome (EDS) and tuberous sclerosis, respectively. We hypothesized that in the patient with tuberous sclerosis, pachydermodactyly is a clinical manifestation of the associated systemic disease, whereas obsessive‐compulsive behavior is probably the main cause in the girl with EDS.