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Giant Congenital Juvenile Xanthogranuloma
Author(s) -
Magana Mario,
Vazquez Ruth,
FernándezDíez Jorge,
FloresVilla Rebeca,
Cazarín Jorge
Publication year - 1994
Publication title -
pediatric dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 73
eISSN - 1525-1470
pISSN - 0736-8046
DOI - 10.1111/j.1525-1470.1994.tb00591.x
Subject(s) - juvenile xanthogranuloma , histiocyte , giant cell , medicine , histiocytosis , juvenile , pathology , langerhans cell histiocytosis , lesion , histiocytosis x , dermatology , biology , disease , genetics
Congenital giant juvenile xanthogranuloma is an uncommon lesion that apparently has benign biologic behavior in most reported patients. In one of our three patients it was necessary to perform histochemical reactions with CD 1 (‐), MAC 387, and electron microscopy to rule out Langerhans cell histiocytosis. The other patients had a typical histologlc picture, with foamy histiocytes and Touton cells in association wtth lymphocytes and eosinophils. Comments about treatment are also made.