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Nutrition in Dystrophic Epidermolysis Bullosa
Author(s) -
Allman Susan,
Haynes Lesley,
MacKin Petrina,
Atherton David J.
Publication year - 1992
Publication title -
pediatric dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 73
eISSN - 1525-1470
pISSN - 0736-8046
DOI - 10.1111/j.1525-1470.1992.tb00337.x
Subject(s) - medicine , epidermolysis bullosa , parenteral nutrition , malnutrition , medical nutrition therapy , gastrostomy , intensive care medicine , pediatrics , dermatology , surgery
In dystrophic epidermolysis bultosa (EB), a combination of diminished food intake and Increased nutritional requirements commonly leads to mainourishment Adequate nutrition in these patterns could pro‐vide many benefits, including Improved growth, accelerated healing, de‐creased susceptibility to infection, and enhanced well‐being. We as‐sessed nutrition status of children with dystrophic EB, and evaluated the benefits of nutritional advice in those who were considered malnour‐ished. The majority of patients had inadequate Intakes of a wide spectrum of nutrients, Including those who appeared to be relatively mildly af‐fected. We were unable to secure persisting substantial Improvements In dietary intake despite thorough counseling. Adequate nutrition In pa‐tients with dystrophic EB depends on active nutritional support starting from birth. The need for more invasive techniques of nourishment, such as nasogastric and gastrostomy feeding, may have to be considered earlier than Is currently the case.