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Cutis Marmorata Telangiectatica Congenita: A Case Report
Author(s) -
Altman Andrew R.,
Tschen Jaime A.,
Wolf John E.
Publication year - 1984
Publication title -
pediatric dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.542
H-Index - 73
eISSN - 1525-1470
pISSN - 0736-8046
DOI - 10.1111/j.1525-1470.1984.tb01121.x
Subject(s) - medicine , livedo reticularis , telangiectasia , dermatology , congenital disorder , pathology , surgery , disease
Cutis marmorata telangiectatica congenita (CMTC) is a rare cutaneous vascular disorder that was first described in 1922 by Van Lohuizen (1). The clinical presentation is one of persistent cutis marmorata, phlebectasia, telangiectasia, and areas of ulcerations. The disorder shows slow clinical improvement over time. Previously, CMTC has also been described as congenital generalized phlebectasia (2–7), congenital phlebectasia (8), nevus vascularis rcticularis (9), congenital livedo reticularis (10), and livedo telangiectatica (11). The following is a case report.