Premium
Hepatic von Meyenburg complex: a trigger of severe portal hypertension
Author(s) -
Yoshida Shuhei,
Kurokohchi Kazutaka,
Ueno Takuya,
Yoshino Morihiko,
Shimada Masahiko,
Masaki Tsutomu
Publication year - 2009
Publication title -
liver international
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.873
H-Index - 110
eISSN - 1478-3231
pISSN - 1478-3223
DOI - 10.1111/j.1478-3231.2008.01903.x
Subject(s) - hepatology , medicine , gastroenterology
To the Editor: Multiple bile duct hamartoma [von Meyenburg complex (VMC)] is a benign liver malformation that includes biliary cystic lesions with congenital hepatic fibrosis causing ductal plate malformations (1–7). It is generally asymptomatic and tends to be identified either at autopsy or during histological examinations (1). We report a very rare case of severe portal hypertension caused by VMC diagnosed by magnetic resonance cholangiopancreatography (MRCP) and histopathology.