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An unusual case of primary systemic amyloidosis
Author(s) -
Ambrosone L.,
Mansi L.,
Salvatore T.,
Marino F.,
Orabona P.,
Rambaldi A.,
Rambaldi P.F.,
Rambaldi M.
Publication year - 1998
Publication title -
journal of the european academy of dermatology and venereology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.655
H-Index - 107
eISSN - 1468-3083
pISSN - 0926-9959
DOI - 10.1111/j.1468-3083.1998.tb00928.x
Subject(s) - medicine , primary systemic amyloidosis , amyloidosis , primary (astronomy) , dermatology , systemic disease , pathology , immunopathology , physics , astronomy
Here we report an unusual case of primary systemic amyloidosis. The cutaneous lesions were polymorphic and included involvement of both external auditory canals. The visceral involvement was covert. Mapping of amyloid deposits was performed using scintigraphy with technetium‐99m (V) dimercaptosuccinic acid ([ 99m Tc (V)] DMSA). Therapy with melpha‐lan, prednisone and colchicine resulted in considerable improvement.