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Cutis marmorata teleangiectatica congenita with segmental distribution
Author(s) -
Boehncke WolfHenning,
Zollner Thomas Matthias,
Kaufmann Roland
Publication year - 1996
Publication title -
journal of the european academy of dermatology and venereology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.655
H-Index - 107
eISSN - 1468-3083
pISSN - 0926-9959
DOI - 10.1111/j.1468-3083.1996.tb00581.x
Subject(s) - medicine , dermis , anatomy , vascular malformation , surgery
Cutis marmorata teleangiectatica congenita (CMTC) is a very rare vascular malformation closely related to port wine stains. It is present at birth, asymmetrical distribution and limb involvement are common. We report here on a 6–month‐old female patient exhibiting the typical clinical appearance of CMTC in a segmental pattern. To date 10 such cases have been reported. CMTC must be distinguished from other vascular malformations with asymmetrical distribution and – in case of a segmental pattern – particularly from unilateral dermatomal superficial teleangiectasia. Because of the tendency of such naevi to spontaneous improvement and localization of vascular dilatations in the dermis and subcutis no treatment was initiated at this point in lime.