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Anaesthesia and the Beckwith‐Wiedemann syndrome
Author(s) -
SUAN CRISTINA,
OJEDA RAFAEL,
GARCÍAPERLA J.L.,
PÉREZTORRES M.C.
Publication year - 1996
Publication title -
pediatric anesthesia
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.704
H-Index - 82
eISSN - 1460-9592
pISSN - 1155-5645
DOI - 10.1111/j.1460-9592.1996.tb00435.x
Subject(s) - medicine , beckwith–wiedemann syndrome , perioperative , inguinal hernia , omphalocele , anesthesia , surgery , hernia , pregnancy , biochemistry , gene expression , chemistry , fetus , dna methylation , gene , genetics , biology
Summary Infants with Beckwith‐Wiedeman syndrome usually present different abnormalities which may require surgical correction. Anaesthetic management may be complicated by abnormal airway anatomy, congenital heart disease and severe hypoglycaemia. Careful preoperative evaluation, perioperative monitoring and suitable choice of anaesthetic technique are required for a successful outcome. We report the perioperative management of a patient with Beckwith‐Wiedemann syndrome presenting for omphalocoele surgery on his first day of life and for bilateral inguinal hernia repair four months later.