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Anaesthesia for Rett syndrome
Author(s) -
DEARLOVE O.R.,
WALKER R.W.M.
Publication year - 1996
Publication title -
pediatric anesthesia
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.704
H-Index - 82
eISSN - 1460-9592
pISSN - 1155-5645
DOI - 10.1111/j.1460-9592.1996.tb00381.x
Subject(s) - medicine , rett syndrome , anesthesia , biochemistry , gene , chemistry
Summary Rett syndrome is a devastingly disabling neurological disease that is only observed in girls. Scoliosis occurs in roughly half the girls and surgery may be required. Anaesthesia is described in three patients. Sudden death may be a feature of the disease which occurred four weeks postoperatively in one case. Although a long QT c interval may be seen, it did not occur in any of our cases.