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Anaesthetic considerations in a child with adrenoleukodystrophy
Author(s) -
NISHINA KAHORU,
MIKAWA KATSUYA,
MAEKAWA NOBUHIRO,
GOTO RYOKICHI,
TANAKA OSAMU,
YAKU HIDEAKI,
OBARA HIDEFUMI
Publication year - 1993
Publication title -
pediatric anesthesia
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.704
H-Index - 82
eISSN - 1460-9592
pISSN - 1155-5645
DOI - 10.1111/j.1460-9592.1993.tb00095.x
Subject(s) - medicine , adrenoleukodystrophy , asymptomatic , halothane , nitrous oxide , adrenal cortex , anesthesia , disease , surgery , peroxisome , receptor
Summary A child with asymptomatic adrenoleukodystrophy (ALD) who uneventfully underwent an operation for undescended testis under halothane‐nitrous oxide anaesthesia is presented. The normal hormonal responses to surgical stress were observed. The potential problems of disorders of the adrenal cortex, the central nervous system, and skeletal muscle associated with the condition are discussed. Rapid‐ACTH test may be a useful method for the evaluation of the adrenocortical function in this disease. It is proposed that a patient with ALD should receive a single dose of steroid regardless of the result of the rapid ACTH test.