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KAPOSIFORM HAEMANGIOENDOTHELIOMA IN AN ADULT FEMALE: CASE REPORT AND LITERATURE REVIEW
Author(s) -
Yang Y.T.,
AlANI S.,
Mills S.
Publication year - 2009
Publication title -
anz journal of surgery
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.426
H-Index - 70
eISSN - 1445-2197
pISSN - 1445-1433
DOI - 10.1111/j.1445-2197.2009.04927_35.x
Subject(s) - lymphangiomatosis , medicine , axilla , differential diagnosis , disease , rare disease , dermatology , pathology , breast cancer , lymphatic system , cancer
Kaposiform haemangioendothelioma (KHE) is a rare vascular tumour that can be locally aggressive. While KHE is commonly associated with Kasabach‐Merritt syndrome and lymphangiomatosis, it predominantly occurs in infancy and early childhood. To date, only ten adult cases of KHE have been reported in literature. We report a case of KHE associated with lymphangiomatosis in the breast and axilla of an 18–year old, otherwise well female. Literatures on the clinical presentations, histopathological findings, differential diagnoses, behaviour and treatment of Kaposiform haemangioendothelioma in adults are reviewed. KHE may occasionally be encountered in adults. Clinical diagnosis and management can be a challenge due to the rarity of this disease. Knowledge of KHE and its associated complications should lead to a prompt diagnosis and early initiation of treatment.