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Rosai–Dorfman disease manifesting as an epibulbar ocular tumour
Author(s) -
de Oliveira Renato CS,
Rigueiro Moacyr,
Vieira Ana C,
de Freitas Denise,
Sato Elcio
Publication year - 2011
Publication title -
clinical and experimental ophthalmology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.3
H-Index - 74
eISSN - 1442-9071
pISSN - 1442-6404
DOI - 10.1111/j.1442-9071.2010.02404.x
Subject(s) - rosai–dorfman disease , medicine , asymptomatic , histiocyte , nodule (geology) , lesion , emperipolesis , biopsy , surgical excision , pathology , wide local excision , dermatology , radiology , paleontology , biology
A bstract The authors report a rare case of extranodal Rosai–Dorfman disease without systemic involvement. A 14‐year‐old girl presented with a slowly progressive, non‐tender, well‐circumscribed, perilimbal nodule in the right eye. Excisional biopsy was performed and histopathologic and immunohistochemical analysis established the diagnosis. Systemic evaluation revealed no other masses. After complete excision of the epibulbar lesion, the patient is asymptomatic and remains on regular follow up with no signs of recurrence. Rosai–Dorfman disease is an infrequent, benign histiocytic disorder that can rarely manifest as an exclusive extranodal mass. We report a case of solitary epibulbar Rosai–Dorfman disease, successfully treated with complete surgical excision of the lesion.