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Management of urethral hemangiomas associated with Klippel–Trenaunay–Weber syndrome by endoscopic sclerotherapy
Author(s) -
Terada Naoki,
Arakaki Ryuichiro,
Okada Yoshiyuki,
Kaneko Yoshiyuki,
Nishimura Kazuo
Publication year - 2007
Publication title -
international journal of urology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.172
H-Index - 67
eISSN - 1442-2042
pISSN - 0919-8172
DOI - 10.1111/j.1442-2042.2007.01571.x
Subject(s) - sclerotherapy , medicine , klippel trenaunay weber syndrome , hemangioma , surgery , klippel trenaunay syndrome , angioma , radiology , vascular disease , muscle hypertrophy , soft tissue
Klippel–Trenaunay–Weber syndrome (KTS) is an unusual congenital anomaly characterized by cutaneous hemangiomas, varicosities and bony hypertrophy of the extremities. Herein the case is reported of a 24‐year‐old man with urethral bleeding from hemangiomas associated with KTS that were successfully managed by endoscopic sclerotherapy. A 23‐G puncture needle was inserted into the bleeding vein to inject a 5% solution of monoethanolamine oleate (Oldamine), which is typically used for sclerotherapy of esophageal vasix. At a 4‐month follow‐up, the patient only had slightly bloodstained urethral discharge, and is doing well. This is the first case reporting endoscopic sclerotherapy for a KTS‐associated urethral hemangioma.