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Malignant retroperitoneal tumor arising in a multicystic dysplastic kidney of a girl with Schinzel–Giedion syndrome
Author(s) -
MATSUMOTO FUMI,
TOHDA AKIRA,
SHIMADA KENJI,
OKAMOTO NOBUHIKO
Publication year - 2005
Publication title -
international journal of urology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.172
H-Index - 67
eISSN - 1442-2042
pISSN - 0919-8172
DOI - 10.1111/j.1442-2042.2005.01213.x
Subject(s) - medicine , girl , multicystic dysplastic kidney , kidney , psychology , developmental psychology
We report the first case of malignant retroperitoneal tumor arising in a multicystic dysplastic kidney of an 8‐year‐old girl with Schinzel‐Giedion syndrome. Although conservative treatment has been regarded as the standard management for asymptomatic multicystic dysplastic kidney, prophylactic surgical removal should be considered for selected children with potential risk of malignancy.