Premium
Diffuse xanthogranulomatous pyelonephritis in a patient with myotonic dystrophy and cerebral palsy
Author(s) -
TAKAYASU HAJIME,
ISHIMARU YUKI,
KISAKI YOSHIYUKI,
NAKAI HIDEO,
UEDA YOSHIHIKO,
IKEDA HITOSHI
Publication year - 2005
Publication title -
international journal of urology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.172
H-Index - 67
eISSN - 1442-2042
pISSN - 0919-8172
DOI - 10.1111/j.1442-2042.2005.01080.x
Subject(s) - medicine , myotonic dystrophy , cerebral palsy , parenchyma , xanthogranulomatous pyelonephritis , pathology , disease , nephrectomy , kidney , physical therapy
Xanthogranulomatous pyelonephritis (XGP), a morphological and clinical variant of chronic pyelonephritis, is an uncommon disease in children. It is characterized by the destruction of the renal parenchyma and replacement by granulomatous tissue containing foamy lipid‐laden macrophages and is classified into diffuse and focal XGP. We present a case of diffuse XGP in a child with myotonic dystrophy complicated by cerebral palsy and discuss the importance of correct diagnosis and preoperative management to reduce inflammation and improve malnutrition associated with the disease.