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Hypoparathyroidism and pseudohypoparathyroidism
Author(s) -
YASUDA TOSHIYUKI,
NIIMI HIROO
Publication year - 1997
Publication title -
pediatrics international
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.49
H-Index - 63
eISSN - 1442-200X
pISSN - 1328-8067
DOI - 10.1111/j.1442-200x.1997.tb03625.x
Subject(s) - pseudohypoparathyroidism , medicine , hyperphosphatemia , hypoparathyroidism , hypomagnesemia , parathyroid hormone , endocrinology , pathophysiology , etiology , calcium , magnesium , materials science , metallurgy
Hypoparathyroidism is a clinical disorder characterized by hypocalcemia and hyperphosphatemia in the absence of renal failure and hypomagnesemia. The causes of hypoparathyroidism can be classified as two groups: (i) insufficient parathyroid hormone (PTH) secretion in relation to the serum calcium level (hypoparathyroidism); and (ii) impaired PTH action (pseudohypoparathyroidism). The main emphasis in this report is to distinguish subgroups based on the etiology and pathophysiology of the various aspects of the disease.