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Atypical hemolytic uremic syndrome
Author(s) -
KAVUKÇU SALIH,
İRKEN GÜLERSU,
OLGUN NUR,
GÜÇLÜ ALEV
Publication year - 1995
Publication title -
pediatrics international
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.49
H-Index - 63
eISSN - 1442-200X
pISSN - 1328-8067
DOI - 10.1111/j.1442-200x.1995.tb03393.x
Subject(s) - medicine , therapeutic plasma exchange , pathogenesis , prednisolone , intensive care medicine , plasmapheresis , fresh frozen plasma , disease , atypical hemolytic uremic syndrome , exchange transfusion , pediatrics , immunology , surgery , complement system , antibody , platelet
The pathogenesis of atypical uremic syndrome (HUS), which is rarely encountered in childhood, is poorly understood and its mortality and morbidity rates are high. A wide variety of therapeutic approaches has been attempted and the literature contains numerous conflicting reports about the results of these approaches. In a case diagnosed as recurrent atypical HUS, pulse methyl prednisolone, fresh frozen plasma infusions and plasma exchange transfusion were used at different stages of the disease with satisfactory response.