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Intravenous γ‐Globulin Therapy in Diamond‐Blackfan Anemia
Author(s) -
Sumimoto Shinichi,
Kawai Masahiko,
Kasajima Yoshiki,
Hamamoto Torata
Publication year - 1992
Publication title -
pediatrics international
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.49
H-Index - 63
eISSN - 1442-200X
pISSN - 1328-8067
DOI - 10.1111/j.1442-200x.1992.tb00947.x
Subject(s) - medicine , diamond–blackfan anemia , globulin , anemia , pediatrics , biochemistry , rna , ribosome , chemistry , gene
Pure red cell aplasia (PRCA) is a rare disorder of erythrocyte production which is believed to have an autoimmune basis in most cases. Diamond‐Blackfan anemia (DBA) is one type of congenital PRCA. Since PRCA has been reported to respond to intravenous γ‐globulin (IVGG) therapy, we administered IVGG to a 2 year old girl with DBA resistant to corticosteroids and observed slight therapeutic effect.