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Treatment of Cystinosis: Decrease in Content of Free Cystine in Leukocytes and Alleviation of Progressive Renal Failure by Treatment with Riboflavin
Author(s) -
Hayasaka Kiyoshi,
Narisawa Kuniaki,
Saitoh Takashi,
Numakura Hirohiko,
Fukuda Kaoru,
Kato Seiichi,
Tayama Toshiyuki,
Tada Keiya
Publication year - 1986
Publication title -
pediatrics international
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.49
H-Index - 63
eISSN - 1442-200X
pISSN - 1328-8067
DOI - 10.1111/j.1442-200x.1986.tb00762.x
Subject(s) - cystinosis , riboflavin , medicine , taurine , cystine , renal function , endocrinology , gastroenterology , biochemistry , enzyme , cysteine , biology , amino acid
Two patients with cystinosis were treated with riboflavin, resulting in a decrease in the content of free cystine and taurine in leukocytes. Riboflavin therapy was not sufficient to improve the renal function; however, the progression of renal failure was alleviated.