Open AccessCONGENITAL NEPHROTIC SYNDROME (FINNISH TYPE)
Author(s) -
Fujinami Mutsuyo,
Hane Yasuyuki,
Ito Katsumi,
Kajita Akira
Publication year - 1985
Publication title -
acta patholigica japonica
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.73
H-Index - 74
ISSN - 0001-6632
DOI - 10.1111/j.1440-1827.1985.tb00594.x
Subject(s) - medicine , nephrotic syndrome , congenital nephrotic syndrome , autopsy , endocardium , pathology , kidney , proteinuria
The case was a one year and four months old boy, who had been diagnosed as congenital nephrotic syndrome on the 4th day of life. He died of septicemia from peritonitis. Large pale kidneys, dilated trunk of pulmonary artery, and thickened left atrial endocardium were observed at autopsy. Renal histology seemed to be compatible with congenital nephrotic syndrome of the Finnish type. Viral antigens of herpes simplex type 1 and varicella‐zoster in paraffin‐embedded sections were proven to be negative. Besides renal change, increased number of pancreatic islets without hypertrophy was noticed. ACTA PATHOL. JPN. 35: 517–525, 1985.