Open AccessSÉZARY SYNDROME: REPORT OF AN AUTOPSY CASE SHOWING SYSTEMIC DEGENERATIVE CHANGE OF THE CONNECTIVE TISSUE
Author(s) -
Tateishi Ryuhei,
Wada Akira,
Fujimoto Yukio,
Inoue Shozo
Publication year - 1965
Publication title -
acta patholigica japonica
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.73
H-Index - 74
ISSN - 0001-6632
DOI - 10.1111/j.1440-1827.1965.tb02891.x
Subject(s) - pathology , autopsy , connective tissue , fibrosis , medicine , edema
Summary An autopsy case of Sezary syndrome is presented. Brief clinical records, major gross and microscopic findings are described. The histological findings characterized by a presence of perivascular edema and fibrosis associated with a proliferation of histiomonocytic cells are so striking as to suggest that this exceptional disease may comprise a distinct clinical and anatomical entity. We consider that Sezary syndrome is a reactive reticulosis that is dependent on a primary degenerative state of the connective tissue.