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A CASE REPORT OF MYOTONIA DYSTROPHICA — ABOUT ITS ELECTROMYOGRAPHIC STUDY —
Author(s) -
Maekawa Magojiro,
Mashiko Naohiko
Publication year - 1960
Publication title -
psychiatry and clinical neurosciences
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.609
H-Index - 74
eISSN - 1440-1819
pISSN - 1323-1316
DOI - 10.1111/j.1440-1819.1960.tb02227.x
Subject(s) - myotonia , myotonic dystrophy , electromyography , atrophy , medicine , chloral hydrate , anesthesia , anatomy , chemistry , audiology , cardiology , physical medicine and rehabilitation
Summary A typical case of myotonia dystrophica was studied electromyographically, and interesting findings were obtained. Electromyograms were recorded by a cathode‐ray oscilloscope with synchronous loud‐speaker using monopolar or bipolar concentric needle electrode. Electromyograms of the respiratory muscles were recorded by 8‐channel‐electroencephalographic apparatus using silver needle electrodes. Results obtained were as follows:1 Typical myotonic activity was obtained in tongue muscle and thenar group. The deflection occurred in both positive and negative directions with amplitude of 400‐700 μV. and duration of 5/60 seconds. And moreover, in monopolar lead, this became monophasic. Characteristic sound was heard. 2 Myotonic activities were observed in muscles attended by no or slight atrophy, and absent from muscles with marked muscular atrophy. Especially, muscular atrophy was typical in M. sternocleidomastoideus, and it showed low amplitude NMU voltage electromyographically. 3 Myotonic activity was induced by moving the inserted needle electrode, or by percussion of the muscle. The reaction first occurred at 11 mA. when electrically stimulated. 4 Myotonic activities were seen during the period of retarded relaxation after forced grasping, diminishing gradually in fashions similar to that of the fibrillation voltage. 5 Myotonia was slightly relieved by administration of quinidine, but dystrophy couldn't be blocked. The duration of myotonic reaction was diminished moderately by the injection of insulin, but slightly prolonged by that of adrenalin.