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Stenosis of pulmonary veins in Down syndrome
Author(s) -
STEWART A. D.,
CALDER A. L.,
NEUTZE J. M.,
JAMES A. H.,
BRANDT P. W. T.
Publication year - 1992
Publication title -
journal of paediatrics and child health
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.631
H-Index - 76
eISSN - 1440-1754
pISSN - 1034-4810
DOI - 10.1111/j.1440-1754.1992.tb02641.x
Subject(s) - medicine , stenosis , intracardiac injection , cardiology , pulmonary vein stenosis , pulmonary hypertension , radiology , pulmonary vein , ablation
Two patients with Down syndrome, intracardiac communications and elevated pulmonary arteriolar resistance presented early in life. Both patients had significant stenosis of pulmonary veins. The progressive nature of the stenosis is illustrated in one patient. Pulmonary venous stenosis in Down syndrome has been recorded only twice before in the literature, and may play a part in the early onset of pulmonary vascular occlusive disease in some patients.