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Small bowel ischaemia in Fabry's disease
Author(s) -
JARDINE D. L.,
FITZPATRICK M. A.,
TROUGHTON W. D.,
TIE A. B. M.
Publication year - 1994
Publication title -
journal of gastroenterology and hepatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.214
H-Index - 130
eISSN - 1440-1746
pISSN - 0815-9319
DOI - 10.1111/j.1440-1746.1994.tb01244.x
Subject(s) - medicine , fabry disease , ischemia , disease , gastroenterology
A patient with previously diagnosed Fabry's disease and a long history of post‐prandial abdominal pain died following small bowel infarction. Post‐mortem demonstrated Fabry's type deposits in the small vessels and nerves supplying the bowel but in addition, a localized atheromatous stenosis of the superior mesenteric artery. In retrospect, his terminal illness and possibly his chronic symptoms were related to the latter finding. Angioplasty to the superior mesenteric artery may have been of benefit. Mesenteric angiography should be considered in patients with chronic post‐prandial pain because large vessel disease may coexist with other a priori pathologies and is imminently treatable.