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Fulminant hepatic failure and acute intravascular haemolysis as presenting manifestations of Wilson's disease in young children
Author(s) -
WALIA B. N. S.,
SINGH S.,
MARWAHA R. K.,
BHUSNURMATH S. R.,
DILAWAR J. B.
Publication year - 1992
Publication title -
journal of gastroenterology and hepatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.214
H-Index - 130
eISSN - 1440-1746
pISSN - 0815-9319
DOI - 10.1111/j.1440-1746.1992.tb01000.x
Subject(s) - medicine , fulminant , haemolysis , fulminant hepatic failure , disease , intensive care medicine , pediatrics , immunology , liver transplantation , transplantation
The cases of three young children (mean age 5.8 years) in whom fulminant hepatic failure and acute intravascular haemolysis were the presenting manifestations of Wilson's disease are reported. Although diagnosis was made ante‐mortem and chelation therapy instituted, the course was relentlessly fatal in all three cases. This presentation of Wilson's disease at such a young age is noteworthy.