Premium
Blastic plasmacytoid dendritic cell neoplasm
Author(s) -
Lim David,
Goodman Hugh,
Rademaker Marius,
Lamont Duncan,
Yung Anthony
Publication year - 2013
Publication title -
australasian journal of dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.67
H-Index - 53
eISSN - 1440-0960
pISSN - 0004-8380
DOI - 10.1111/j.1440-0960.2011.00848.x
Subject(s) - medicine , plasmacytoid dendritic cell , asymptomatic , hematologic malignancy , neoplasm , bone marrow , dendritic cell , malignancy , transplantation , pathology , bone marrow transplantation , immunology , immune system
Blastic plasmacytoid dendritic cell neoplasm (BPDCN) is a rare haematological malignancy that originates from the precursors of plasmacytoid dendritic cells. It commonly presents with findings isolated to the skin although it usually progresses to a leukaemic phase. It has a poor prognosis but is curable, particularly in younger patients treated with allogeneic bone marrow transplantation. We report a case of a 79‐year old man who had 6 months of progressive, asymptomatic BPDCN manifestations limited to the skin, before developing a leukaemic phase.
Accelerating Research
Robert Robinson Avenue,
Oxford Science Park, Oxford
OX4 4GP, United Kingdom
Address
John Eccles HouseRobert Robinson Avenue,
Oxford Science Park, Oxford
OX4 4GP, United Kingdom