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Liver transplant in an infant with bilateral cystic neuroblastoma complicated by hepatic metastases and life‐threatening consumption coagulopathy
Author(s) -
Haberal Mehmet,
Ozcay Figen,
Sevmis Sinasi,
Karakayali Hamdi,
Moray Gokhan,
Torgay Adnan,
Coskun Mehmet,
Demirhan Beyhan,
Sarialioglu Faik,
Arslan Gulnaz
Publication year - 2008
Publication title -
pediatric transplantation
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.457
H-Index - 69
eISSN - 1399-3046
pISSN - 1397-3142
DOI - 10.1111/j.1399-3046.2008.00887.x
Subject(s) - medicine , coagulopathy , neuroblastoma , liver transplantation , chemotherapy , liver disease , surgery , kasabach–merritt syndrome , transplantation , genetics , biology , cell culture
Here we report a patient with stage‐4 bilateral cystic adrenal neuroblastomas with disseminated liver metastases and consumption coagulopathy who underwent liver transplant. Our patient was initially diagnosed with infantile hepatic hemangioendothelioma and bleeding into the adrenal glands secondary to consumption coagulopathy (Kasabach‐Merritt syndrome). Liver transplant was performed as a life‐saving procedure under this diagnosis. We discuss this unique patient because of the diagnostic pitfalls of this rare disease and the successful clinical outcome after LT and subsequent chemotherapy for neuroblastoma.