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Successful cardiac transplantation in Barth syndrome – single‐centre experience of four patients
Author(s) -
Mangat Jasveer,
LunWood Tracy,
Rees Philip,
Elliott Martin,
Burch Michael
Publication year - 2007
Publication title -
pediatric transplantation
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.457
H-Index - 69
eISSN - 1399-3046
pISSN - 1397-3142
DOI - 10.1111/j.1399-3046.2006.00629.x
Subject(s) - medicine , transplantation , heart transplantation , surgery , cardiology
We describe four patients with Barth syndrome who have undergone successful orthotopic heart transplantation. Patients are one, seven, 12.5 and 14.7 yr post‐transplantation. One episode of severe infection occurred. Renal dysfunction and coronary allograft vasculopathy do not appear accelerated over non‐Barth patients. Despite withholding purine synthesis inhibitors, these patients have not demonstrated an increased rate of rejection.