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Liver transplantation for a hilar inflammatory myofibroblastic tumor
Author(s) -
Dasgupta D.,
Guthrie A.,
McClean P.,
Davison S.,
Luntley J.,
Rajwal S.,
Lodge J. P. A.,
Prasad K. R.,
Wyatt J. I.,
Stringer M. D.
Publication year - 2004
Publication title -
pediatric transplantation
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.457
H-Index - 69
eISSN - 1399-3046
pISSN - 1397-3142
DOI - 10.1111/j.1399-3046.2004.00206.x
Subject(s) - medicine , hilum (anatomy) , liver transplantation , portal vein , obstructive jaundice , porta hepatis , transplantation , occlusion , inflammatory pseudotumor , radiology , pathology , surgery , lesion
A 7‐yr‐old boy presented with obstructive jaundice secondary to an inflammatory myofibroblastic tumor centered on the hepatic hilum and extending into the liver. The tumor was further complicated by portal vein phlebitis and occlusion. Attempted resection of the tumor with portal vein reconstruction and bilioenteric drainage was unsuccessful and he required urgent orthotopic liver transplantation. In contrast to more peripheral inflammatory myofibroblastic tumors in the liver, hilar lesions are locally aggressive, causing occlusive portal phlebitis and biliary obstruction. Successful management may include the need for liver transplantation.
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