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Telangiectasia macularis eruptiva perstans with an associated myeloproliferative disorder
Author(s) -
Martin Lucy K.,
Romanelli Paolo,
Ahn Yeon Soong,
Kirsner Robert S.
Publication year - 2004
Publication title -
international journal of dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.677
H-Index - 93
eISSN - 1365-4632
pISSN - 0011-9059
DOI - 10.1111/j.1365-4632.2004.02249.x
Subject(s) - medicine , dermatology , telangiectasia , refractory (planetary science) , thrombocytosis , myeloproliferative disorders , platelet , pathology , physics , astrobiology
Telangiectasia macularis eruptiva perstans (TMEP) is a cutaneous form of mastocytosis. It has been rarely associated with an underlying myeloproliferative disorder. We report the case of a patient, while receiving treatment for thrombocytosis, with both platelet production and function inhibitors presented with TMEP. TMEP is often refractory to therapy; however, our patient responded to treatment with PUVA.