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Papillon‐Lefévre Syndrome
Author(s) -
El Darouti M.A.,
Al Raubaie S. M.,
Eiada M. A.
Publication year - 1988
Publication title -
international journal of dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.677
H-Index - 93
eISSN - 1365-4632
pISSN - 0011-9059
DOI - 10.1111/j.1365-4362.1988.tb02344.x
Subject(s) - medicine , palmoplantar keratoderma , dermatology , hyperkeratosis , retinoid , dyskeratosis , genetics , biology , retinoic acid , gene
Papillon‐Lefévre syndrome is a rare autosomal recessive disorder of palmoplantar keratinization in which there is a unique association of the palmoplantar hyperkeratosis and premature loss of both deciduous and permanent teeth. We report three patients with papillon‐lefévre syndrome who showed a remarkable degree of improvement after treatment with an oral retinoid.