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Bazex Syndrome: Follicular Atrophoderma and Basal Cell Epitheliomas
Author(s) -
Mehta V. R.,
Potuar R.
Publication year - 1985
Publication title -
international journal of dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.677
H-Index - 93
eISSN - 1365-4632
pISSN - 0011-9059
DOI - 10.1111/j.1365-4362.1985.tb05518.x
Subject(s) - medicine , nevoid basal cell carcinoma syndrome , dermatology , pathology , histopathology , basal cell , trunk , hair follicle , basal cell carcinoma , biology , ecology
A dominant inheritance leading to development of nevoid basal cell epitheliomas on the face and follicular atrophoderma on the extremities constitute the two constant manifestations of Bazex syndrome. A patient with both manifestations on the trunk who fulfilled all the criteria for a diagnosis of nevoid basal cell epitheliomas is described. Histopathology of the basal ceil cancer corresponded to that of the fibroepithelial tumor, thus differing from the more common nodular and trichoepitheliomatous persentations. Difficulty in associating the atrophoderrna with a hair follicle (histologically) arises because the latter ceases to exist as a functional unit.