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Dermatofibrosarcoma Protuberans
Author(s) -
Gutierrez Guillermo,
Ospina Julio E.,
Baez Nohora Elizabeth,
Escorcia Eva Klauss,
Gutierrez Rafael
Publication year - 1984
Publication title -
international journal of dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.677
H-Index - 93
eISSN - 1365-4632
pISSN - 0011-9059
DOI - 10.1111/j.1365-4362.1984.tb03200.x
Subject(s) - dermatofibrosarcoma protuberans , medicine , aponeurosis , incidence (geometry) , soft tissue , dermatofibrosarcoma , dermatology , pathology , surgery , physics , optics
In view of the important clinicopathologic, evolutional, and ultrastructural characteristics of dermatofibrosarcoma Protuberans, a review was made of 30 patients seen during the last 25 years in Colombia's Instituto Nacional de Cancerologia. The incidence is low, accounting for 0.06% of all malignant tumors and 1.17% of all soft‐parts sarcomas. The series comprises 19 women and 11 men, with the highest incidence found between ages of 30 and 50 years, although the study includes two children, ages 8 and 13. The chest was the most common site. Forty percent of the lesions were multinodular, and 23.3% showed ulceration. Histologic appearance is characterized in all cases by fusiform cells arranged like spokes around an empty hub. The fibroblastic origin was ascertained by electron‐microscopic studies. The treatment used was broad surgical excision, removing tissue down to the aponeurosis to avoid recurrence.