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The dental management of a patient with hyperimmunoglobulinemia E syndrome: a case report
Author(s) -
MCAULIFFE N. J.,
HUNTER M. L.,
KAU C. H.,
HUNTER B.,
KNOX J.
Publication year - 2005
Publication title -
international journal of paediatric dentistry
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.183
H-Index - 62
eISSN - 1365-263X
pISSN - 0960-7439
DOI - 10.1111/j.1365-263x.2005.00596.x
Subject(s) - medicine , dentition , dental anomalies , intervention (counseling) , connective tissue , dentistry , connective tissue disorder , surgery , pathology , psychiatry
Summary. Hyperimmunoglobulinemia E recurrent infection syndrome (also known as Job's syndrome) is a rare multi‐system primary immunological disorder in which non‐immunological abnormalities of the dentition, bones and connective tissue are also seen. A previous study has reported the occurrence of dental abnormalities in three‐quarters of individuals diagnosed as suffering from this condition. The present authors report the case of a boy whose prolonged retention of the primary dentition was associated with delayed eruption of permanent teeth. They emphasize the need for early intervention in order to help minimize later orthodontic problems.