Premium
Malignant schwannoma of the stomach in a patient with von Recklinghausen's disease
Author(s) -
CROKER J. R.,
GREENSTEIN R. J.
Publication year - 1979
Publication title -
histopathology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.626
H-Index - 124
eISSN - 1365-2559
pISSN - 0309-0167
DOI - 10.1111/j.1365-2559.1979.tb02983.x
Subject(s) - neurofibromatosis , schwannoma , medicine , gastrointestinal tract , stomach , autopsy , malignancy , neurofibroma , pathology , plexiform neurofibroma , disease , malignant disease , cancer , gastroenterology
A patient with von Recklinghausen's disease died with a malignant schwannoma of the stomach and was found at autopsy to have neurofibromatosis of the gastrointestinal tract, a plexiform neurofibroma of the myocardium and a phaechromocytoma. Malignancy of the gastrointestinal tract in von Recklinghausen's disease is rare, and this case highlights the difficulties in histological diagnosis of malignant nerve sheath tumours.