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Cardiac surgery in patients with haemophilia B: a case report and review of the literature
Author(s) -
KRAKOW E. F.,
WALKER I.,
LAMY A.,
ANDERSON J. A. M.
Publication year - 2009
Publication title -
haemophilia
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.213
H-Index - 92
eISSN - 1365-2516
pISSN - 1351-8216
DOI - 10.1111/j.1365-2516.2008.01918.x
Subject(s) - medicine , haemophilia , cardiac surgery , valvular heart disease , disease , haemophilia a , surgery , multidisciplinary approach , multidisciplinary team , haemophilia b , aortic valve replacement , intensive care medicine , general surgery , pediatrics , cardiology , nursing , social science , stenosis , sociology
Summary. Cardiac surgery for coronary heart disease, and for calcific and degenerative valvular heart disease, will likely become more frequent with an ageing haemophilia population. Our report describes the successful management of an individual with mild haemophilia B undergoing elective aortic valve replacement using a continuous infusion of recombinant factor IX. Emphasis is placed on the multidisciplinary coordination of care required across three hospital sites to ensure an uncomplicated peri‐ and postoperative course. We also provide a review of the current literature on cardiac surgery in patients with haemophilia B.