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Liver haemorrhage in haemophilia – a case report and review of the literature
Author(s) -
HAMILTON M.,
FRENCH W.,
RHYMES N.,
COLLINS P.
Publication year - 2006
Publication title -
haemophilia
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.213
H-Index - 92
eISSN - 1365-2516
pISSN - 1351-8216
DOI - 10.1111/j.1365-2516.2006.01291.x
Subject(s) - medicine , haemophilia , haemophilia a , complication , pediatrics , disseminated intravascular coagulation , severe bleeding , coagulopathy , surgery , intensive care medicine
Summary. We present two patients with severe haemophilia A, who presented with haemorrhagic shock, secondary to a liver haematoma in the neonatal period. Both required emergency treatment and diagnosis of the hereditary coagulation defect. Major organ bleeding in severe haemophilia A in the newborn period is rare, and this unusual complication is not well recognized. Failure to recognize that the bleeding is due to a bleeding disorder, particularly in the absence of a family history, may lead to delay in appropriate management.