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MALE PSEUDOHERMAPHRODITISM DUE TO PARTIAL END‐ORGAN INSENSITIVITY TO ANDROGENS
Author(s) -
BARRAGRY J. M.,
MAKIN H. L. J.,
MORRIS D. V.,
TRAFFORD D. J. H.,
MASON A. STUART
Publication year - 1977
Publication title -
clinical endocrinology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.055
H-Index - 147
eISSN - 1365-2265
pISSN - 0300-0664
DOI - 10.1111/j.1365-2265.1977.tb01305.x
Subject(s) - male pseudohermaphroditism , virilization , endocrinology , medicine , pseudohermaphroditism , testosterone (patch) , hormone , biology , androgen
SUMMARY A 46XY individual with incomplete male pseudohermaphroditism was studied. The phenotype was distinctive, with a masculine habitus despite a small phallus, gynaecomastia and diminished virilization. Plasma levels of testosterone, oestrogens, gonadotrophins and sex‐hormone binding globulin were elevated. It is proposed that this syndrome is a variant of Type I incomplete male pseudohermaphroditism.