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Wegener’s granulomatosis: a new entity in the growing differential diagnosis of Degos’ disease
Author(s) -
Guhl G.,
DiazLey B.,
Delgado Y.,
Daudén E.,
Fraga J.,
GarcíaDiez A.
Publication year - 2009
Publication title -
clinical and experimental dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.587
H-Index - 78
eISSN - 1365-2230
pISSN - 0307-6938
DOI - 10.1111/j.1365-2230.2008.02953.x
Subject(s) - pathognomonic , medicine , differential diagnosis , dermatology , pathology , vasculitis , purpura (gastropod) , disease , wegener granulomatosis , ecology , biology
Summary Wegener’s granulomatosis (WG) is a multisystemic vasculitis, with skin involvement in 14% of cases and with palpable purpura, subcutaneous nodules and necrotic papules as the common features. 1 We present a patient diagnosed with WG who had multiple whitish papules similar to those of malignant atrophic papulosis (Degos’ disease), which appeared during a flare of his disease. Lesions of malignant atrophic papulosis are said to be pathognomonic; nevertheless, various diseases with similar clinical lesions have been described. To our knowledge, this is the first reported case of such lesions in a patient with WG, and we suggest WG should be included in the differential diagnosis of Degos’ disease.