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Myelofibrosis in a patient with pachydermoperiostosis
Author(s) -
Bachmeyer C.,
Blum L.,
Cadranel J.F.,
Delfraissy J.F.
Publication year - 2005
Publication title -
clinical and experimental dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.587
H-Index - 78
eISSN - 1365-2230
pISSN - 0307-6938
DOI - 10.1111/j.1365-2230.2005.01891.x
Subject(s) - myelofibrosis , medicine , dermatology , hypertrophic osteoarthropathy , spinal osteoarthropathy , pathology , bone marrow
Summary Pachydermoperiostosis (idiopathic or primary hypertrophic osteoarthropathy) is a rare condition of unknown origin involving the skin and the skeleton, with an autosomal dominant transmission. We report a case of anaemia in a patient with pachydermoperiostosis indicating myelofibrosis, and review the literature and the pathogenetic mechanisms.