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Extensive naevus comedonicus in a child with Alagille syndrome
Author(s) -
WOODS K.A.,
LARCHER V.F.,
HARPER J.I.
Publication year - 1994
Publication title -
clinical and experimental dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.587
H-Index - 78
eISSN - 1365-2230
pISSN - 0307-6938
DOI - 10.1111/j.1365-2230.1994.tb01149.x
Subject(s) - alagille syndrome , medicine , dermatology , cholestasis
Summary Naevus comedonicus is a rare condition, thought to be a hamartoma in which cells of the pilosebaceous unit fail to develop appropriately. 1 Although it is usually an isolated phenomenon, it has been associated with other defects, including those of the skeletal, ocular and central nervous system. 2 A girl with this condition is described who also had Alagille syndrome (arteriohepatic dysplasia), a previously unreported association.