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Unusual manifestations of primary cutaneous amyloidosis in association with Raynaud's phenomenon and livedo reticularis
Author(s) -
NALDI L.,
MARCHESI L.,
LOCATI F.,
BERTI E.,
CAINELLI T.
Publication year - 1992
Publication title -
clinical and experimental dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.587
H-Index - 78
eISSN - 1365-2230
pISSN - 0307-6938
DOI - 10.1111/j.1365-2230.1992.tb00177.x
Subject(s) - livedo reticularis , medicine , dermatology , amyloidosis , raynaud's disease , raynaud disease , pathology , disease
Summary A patient with unusual manifestations of primary cutaneous amyloidosis, including macules, papules, oedematous plaques and urticarial lesions is described. Raynaud's phenomenon and livedo reticularis were an associated finding. During the acute phase, single doses of systemic corticosteroids resulted in an impressive, long‐lasting improvement in cutaneous manifestations.