Premium
Erythrodermic follicular mucinosis
Author(s) -
FAIRRIS G. M.,
KIRKHAM N.,
GOODWIN P. G.,
LEPPARD B. J.,
WHITE J. F.
Publication year - 1987
Publication title -
clinical and experimental dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.587
H-Index - 78
eISSN - 1365-2230
pISSN - 0307-6938
DOI - 10.1111/j.1365-2230.1987.tb01857.x
Subject(s) - medicine , pathology , scalp , dermatology , mucinosis , follicular phase , follicular cyst , mycosis fungoides , cyst , lymphoma
Summary A unique case of follicular mucinosis is described with erythroderma, boggy, purulent plagues on the scalp ami face, widespread alopecia, purulent paronychia and nail loss. The illness was associated with an eosinophilia, an excess of abnormally shaped ‘activated T cells’ in the peripheral blood and responded to oral steroid therapy. Follicular mucinosis is characterized by an accumulation of acid mucopolysaccharides in the sebaceous glands and the outer root sheath of hair follicles. Three clinical variants are recognized 1, 2 . The most common presentation is that of lesions confined to the head and neck which are usually indurated plaques with prominent follicular openings and obvious alopecia on hairy sites. A second group have widespread lesions which may be discrete follicuiar papules or ill‐defined plaques formed by the confluence of numerous popular lesions. The skin is usually mildly indurated and scaly. The third group has widespread plaques of follicular mucinosis and a coexisting reticulosis which is usually mycosis fungoides. Rare presentations of follicular mucinosis include light‐induced follicular mucinosis 3 , cystic changes on the face4 and generalized follicular mucinosis 5,6 . There have been no previous descriptions of erythro‐dermic follicular mucinosis.