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The cutaneous manifestations of the Klippel‐Trenaunay‐Weber syndrome
Author(s) -
VILJOEN D.,
SAXE N.,
PEARNJ J.,
BEIGHTON P.
Publication year - 1987
Publication title -
clinical and experimental dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.587
H-Index - 78
eISSN - 1365-2230
pISSN - 0307-6938
DOI - 10.1111/j.1365-2230.1987.tb01845.x
Subject(s) - eponym , medicine , klippel trenaunay weber syndrome , dermatology , complication , natural history , surgery , physics , acoustics , muscle hypertrophy
Summary The Klippel‐Trenaunay‐Weber syndrome (KTWS) is the widely accepted eponym for the condition of angioosteohypertrophy. The clinical features of limb overgrowth and various vascular malformations have been previously well‐described, but the spectrum of dermatological manifestations of the KTWS is less well‐documented. For this reason we have evaluated the natural history of the cutaneous lesions in 20 affected individuals. It has emerged that the hitherto unreported problem of aseptic cellulilis is a frequent and potentially severe complication in the KTWS.