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Primary nodal marginal zone B‐cell lymphoma: clinical features and prognostic assessment of a rare disease
Author(s) -
Arcaini Luca,
Paulli Marco,
Burcheri Sara,
Rossi Andrea,
Spina Michele,
Passamonti Francesco,
Lucioni Marco,
Motta Teresio,
Canzonieri Vincenzo,
Montanari Mauro,
Bonoldi Emanuela,
Gallamini Andrea,
Uziel Lilj,
Crugnola Monica,
Ramponi Antonio,
Montanari Francesca,
Pascutto Cristiana,
Morra Enrica,
Lazzarino Mario
Publication year - 2007
Publication title -
british journal of haematology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.907
H-Index - 186
eISSN - 1365-2141
pISSN - 0007-1048
DOI - 10.1111/j.1365-2141.2006.06437.x
Subject(s) - medicine , international prognostic index , univariate analysis , stage (stratigraphy) , follicular lymphoma , lymphoma , multivariate analysis , b symptoms , gastroenterology , marginal zone , surgery , survival analysis , oncology , rituximab , immunology , b cell , antibody , biology , paleontology
Summary This study defined the clinical features and assessed the prognosis of 47 patients (17 males, 30 females, median age 63 years) with primary nodal marginal zone B‐cell lymphoma. Forty‐five per cent had stage IV disease. Hepatitis C virus serology was positive in 24%. According to the Follicular Lymphoma International Prognostic Index (FLIPI), 33% were classified as low‐risk, 34% as intermediate‐risk, and 33% as high‐risk. The 5‐year overall survival (OS) was 69%. In univariate analysis worse OS was associated with: FLIPI ( P = 0·02), age > 60 years ( P = 0·05) and raised lactate dehydrogenase ( P = 0·05). In multivariate analysis, only FLIPI predicted a worse OS ( P = 0·02).