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Childhood linear IgA disease in association with autoimmune lymphoproliferative syndrome
Author(s) -
Wong C.S.M.,
Arkwright P.D.,
Rieuxlaucat F.,
Cant A.J.,
Stevens R.F.,
Judge M.R.
Publication year - 2004
Publication title -
british journal of dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 2.304
H-Index - 179
eISSN - 1365-2133
pISSN - 0007-0963
DOI - 10.1111/j.1365-2133.2004.05850.x
Subject(s) - lymphoproliferative disease , autoimmune lymphoproliferative syndrome , medicine , autoimmune disease , disease , lymphoproliferative disorders , immunology , immunopathology , lymphoma , pathology , biology , genetics , apoptosis , programmed cell death , fas receptor
Summary A child is described who had the signs of autoimmune lymphoproliferative syndrome from an early age and later developed a blistering dermatosis that was shown to be childhood linear IgA disease.
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