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Solitary congenital self‐healing reticulohistiocytosis
Author(s) -
BERNSTEIN E.F.,
RESNIK K.S.,
LOOSE J.H.,
HALCIN C.,
KAUH Y.C.
Publication year - 1993
Publication title -
british journal of dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 2.304
H-Index - 179
eISSN - 1365-2133
pISSN - 0007-0963
DOI - 10.1111/j.1365-2133.1993.tb03175.x
Subject(s) - medicine , histiocytosis , nodule (geology) , differential diagnosis , langerhans cell histiocytosis , pathology , congenital disorder , histopathological examination , dermatology , surgery , disease , biology , paleontology
Summary Congenital self‐healing reticulohistiocytosis (CSHR) was first described in 1973 by Hashimoto and Pritzker. Since then, both multiple and solitary forms have been described. We report a further case of solitary congenital self‐healing reticulohistiocytosis. CSHR is a rare disorder which frequently presents a diagnostic dilemma in the newborn. Nodular forms of systemic Langerhans cell histiocytosis may present in a manner similar to CSHR. Because their differentiation on histopathological grounds is impossible, physical examination, laboratory investigations, and follow‐up are necessary to ensure a lack of systemic involvement. Although previously thought to represent a rare variant of CSHR, solitary lesions of CSHR account for almost 25% of reported cases. A review of the literature relating to solitary CSHR, and a consideration of the differential diagnosis of a solitary congenital nodule, are also presented.